Macrodactyly: decision-making and surgery timing

Marybeth Ezaki, Terri Beckwith, Scott N Oishi

Research output: Contribution to journalReview article

Abstract

Macrodactyly is a rare condition in which fingers, hands or limb growth is unregulated, resulting in overgrowth of tissues in the affected extremities. It is critical to properly assess these extremities for signalling pathway, psychological impact and potential surgical intervention, to achieve the best possible outcome for each patient. Treatment approaches can vary, and patient and family expectations weigh heavily on care complexity. Common surgical procedures may include epiphysiodeses, osteotomies, debulking procedures, carpal tunnel releases, toe transfers and amputations. The selection and timing of these surgeries is a vital component of the approach, as delayed healing and excessive scarring may occur. The purpose of this review is to assist in the navigation of decision-making and surgical timing for patients presenting with overgrowth manifesting itself as macrodactyly.

LanguageEnglish (US)
Pages32-42
Number of pages11
JournalJournal of Hand Surgery: European Volume
Volume44
Issue number1
DOIs
StatePublished - Jan 1 2019

Fingerprint

Decision Making
Extremities
Toes
Osteotomy
Wrist
Amputation
Fingers
Cicatrix
Hand
Psychology
Growth
Megalodactyly
Therapeutics

Keywords

  • Macrodactyly
  • overgrowth
  • paediatric orthopaedics
  • patient care
  • PIK3CA
  • surgical care

ASJC Scopus subject areas

  • Surgery

Cite this

Macrodactyly : decision-making and surgery timing. / Ezaki, Marybeth; Beckwith, Terri; Oishi, Scott N.

In: Journal of Hand Surgery: European Volume, Vol. 44, No. 1, 01.01.2019, p. 32-42.

Research output: Contribution to journalReview article

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